What is polyostotic fibrous dysplasia?

What is polyostotic fibrous dysplasia?

Polyostotic fibrous dysplasia — More than one bone is involved. It can affect more than one bone within the same limb or multiple bones throughout the body. This form of the condition is usually more severe. For this reason, it is typically discovered earlier in life.

What does fibrous dysplasia look like on xray?

Plain radiograph The appearance of fibrous dysplasia is usually smooth and homogeneous with endosteal scalloping and cortical thinning 5. The borders are well defined and the cortex is usually intact but thinned due to the expansive nature of the lesion 5. Other features include: ground-glass matrix.

Does fibrous dysplasia stop growing?

Fibrous dysplasia is a tumor-like disorder of the bone caused by abnormal osteogenesis and its lesions generally stop growing when patients reach adulthood.

What causes polyostotic fibrous dysplasia?

Fibrous dysplasia is linked to a gene mutation present in certain cells that produce bone. The mutation results in the production of immature and irregular bone tissue. Most often the irregular bone tissue (lesion) is present at a single site on one bone.

What does fibrous dysplasia look like?

Fibrous dysplasia usually occurs in children ages 3 to 15, but it sometimes is not diagnosed until adulthood. The exact cause of fibrous dysplasia is not known, but it is not passed down through families. Symptoms may include bone pain and deformity, a waddling walk, and scoliosis.

How long can you live with fibrodysplasia?

The median estimated lifespan of individuals with FOP is approximately 56 years of age.

What mimics fibrous dysplasia?

Abstract. Fibrous dysplasia can be monostotic or, less commonly, polyostotic. The imaging features of polyostotic fibrous dysplasia may closely mimic those of metastatic bone disease, Paget disease, or enchondromatosis (Ollier disease).

Can you live a normal life with fibrous dysplasia?

Individuals with milder forms of FD often live normal, otherwise healthy lives. The prognosis is as widely variable as the disorder itself, and is based on the bones affected, whether other structures such as nerves are affected, and whether fractures occur.

What are the signs and symptoms of fibrous dysplasia?

What are the symptoms of fibrous dysplasia?

• A waddling walk.
• Bone deformity.
• Bone fractures.
• Bone pain (which happens when the fibrous tissue expands in the bone)
• Scoliosis (a sideways curve of the spine)

Is fibrous dysplasia a tumor?

Fibrous dysplasia is a benign fibroosseous bone tumor that accounts for 5% to 10% of benign bone tumors.

Is fibrous dysplasia a disability?

Fibrous dysplasia is a condition where primitive bone cells proliferate inside the bone, weakening its structure and causing pain and disability.

Does fibrous dysplasia make you tired?

People living with fibrous dysplasia may have no signs or symptoms at all, but for others living with FD signs and symptoms may include: Fatigue, particularly in young children. Pain and weakness in the areas affected. Fractures or breaks.